Diagnóstico y manejo de las complicaciones cardiacas en el paciente con distrofia muscular de Duchenne

Duchenne muscular dystrophy is the most common and severe muscular dystrophy in childhood. As the disease progresses, there is evidence of cardiac muscle involvement with the presence of dilated cardiomyopathy and hypertrophic or restrictive cardiomyopathy, leading to heart failure. Currently, there is no curative treatment for Duchenne muscular dystrophy or its cardiovascular complications. However, the use of glucocorticoids, physical rehabilitation, non-invasive mechanical ventilation, and multidisciplinary management with a cardiorespiratory and orthopedic focus have been shown to modify the natural history of the disease. This article provides a synthesis of the diagnosis and treatment of patients diagnosed with Duchenne muscular dystrophy who present cardiovascular complications.